{"created":"2023-05-15T16:30:23.449847+00:00","id":1498,"links":{},"metadata":{"_buckets":{"deposit":"c46fad96-a14a-4ca5-a9b2-d2c74f71baba"},"_deposit":{"created_by":2,"id":"1498","owners":[2],"pid":{"revision_id":0,"type":"depid","value":"1498"},"status":"published"},"_oai":{"id":"oai:nagasaki-u.repo.nii.ac.jp:00001498","sets":["8:9"]},"author_link":["7126","7112","7109","7113","7106","7110","7108","7116","7111","7123","7125","7114","7115","7124","7122","7117","7120","7118","7121","7119","7107"],"item_2_biblio_info_6":{"attribute_name":"書誌情報","attribute_value_mlt":[{"bibliographicIssueDates":{"bibliographicIssueDate":"2018-07-06","bibliographicIssueDateType":"Issued"},"bibliographicIssueNumber":"23","bibliographicPageEnd":"3478","bibliographicPageStart":"3473","bibliographicVolumeNumber":"57","bibliographic_titles":[{"bibliographic_title":"Internal Medicine"}]}]},"item_2_description_4":{"attribute_name":"抄録","attribute_value_mlt":[{"subitem_description":"A 56-year-old Japanese woman with muscle weakness, increased creatine kinase and aldolase levels, \nand characteristic cutaneous lesions was diagnosed with anti-melanoma differentiation-associated gene 5 antibody \n(anti-MDA5 antibody)-positive dermatomyositis. She also had interstitial lung disease (ILD). \nAfter corticosteroid and tacrolimus combination therapy was started,\n bicytopenia and elevated serum ferritin and trans-aminase emerged. \nBecause the bone marrow tissues were hypoplastic with hemophagocytes, \nshe was diagnosed with concomitant autoimmune-associated hemophagocytic syndrome (HPS). \nIntravenous cyclophosphamide pulse therapy and plasmapheresis were performed. \nThe laboratory findings indicated improved abnormalities, and the ILD did not progress.\n Anti-MDA5 antibody-positive dermatomyositis can be complicated by HPS.","subitem_description_type":"Abstract"}]},"item_2_description_63":{"attribute_name":"引用","attribute_value_mlt":[{"subitem_description":"Internal Medicine, 57(23), pp.3473-3478; 2018","subitem_description_type":"Other"}]},"item_2_publisher_33":{"attribute_name":"出版者","attribute_value_mlt":[{"subitem_publisher":"日本内科学会"}]},"item_2_relation_12":{"attribute_name":"DOI","attribute_value_mlt":[{"subitem_relation_type":"isIdenticalTo","subitem_relation_type_id":{"subitem_relation_type_id_text":"10.2169/internalmedicine.1121-18","subitem_relation_type_select":"DOI"}}]},"item_2_rights_13":{"attribute_name":"権利","attribute_value_mlt":[{"subitem_rights":"c2018 The Japanese Society of Internal Medicine. The Internal Medicine is an Open Access journal distributed under the Creative Commons Attribution-NonCommercial-NoDerivatives 4.0 International License. To view the details of this license, please visit (https://creativecommons.org/licenses/by-nc-nd/4.0/)."}]},"item_2_source_id_7":{"attribute_name":"ISSN","attribute_value_mlt":[{"subitem_source_identifier":"09182918","subitem_source_identifier_type":"ISSN"}]},"item_2_source_id_8":{"attribute_name":"EISSN","attribute_value_mlt":[{"subitem_source_identifier":"13497235","subitem_source_identifier_type":"ISSN"}]},"item_2_text_62":{"attribute_name":"出版者別言語","attribute_value_mlt":[{"subitem_text_value":"Japanese Society of Internal Medicine"}]},"item_2_version_type_16":{"attribute_name":"著者版フラグ","attribute_value_mlt":[{"subitem_version_resource":"http://purl.org/coar/version/c_970fb48d4fbd8a85","subitem_version_type":"VoR"}]},"item_creator":{"attribute_name":"著者","attribute_type":"creator","attribute_value_mlt":[{"creatorNames":[{"creatorName":"Fujita, Yuya"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"Fukui, Shoichi"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"Suzuki, Takahisa"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"Ishida, Midori"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"Endo, Yushiro"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"Tsuji, Sousuke"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"Takatani, Ayuko"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"Igawa, Takashi"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"Shimizu, Toshimasa"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"Umeda, Masataka"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"Sumiyoshi, Remi"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"Nishino, Ayako"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"Koga, Tomohiro"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"Kawashiri, Shin-ya"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"Iwamoto, Naoki"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"Ichinose, Kunihiro"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"Tamai, Mami"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"Nakamura, Hideki"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"Origuchi, Tomoki"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"Abe, Kuniko"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"Kawakami, Atsushi"}],"nameIdentifiers":[{}]}]},"item_files":{"attribute_name":"ファイル情報","attribute_type":"file","attribute_value_mlt":[{"accessrole":"open_date","date":[{"dateType":"Available","dateValue":"2020-12-18"}],"displaytype":"detail","filename":"IntMed57_3473.pdf","filesize":[{"value":"1.8 MB"}],"format":"application/pdf","licensetype":"license_note","mimetype":"application/pdf","url":{"label":"IntMed57_3473.pdf","url":"https://nagasaki-u.repo.nii.ac.jp/record/1498/files/IntMed57_3473.pdf"},"version_id":"1446159f-47f3-46bd-a718-1aa011f1297a"}]},"item_keyword":{"attribute_name":"キーワード","attribute_value_mlt":[{"subitem_subject":"Anti-MDA5 antibody-positive dermatomyositis","subitem_subject_scheme":"Other"},{"subitem_subject":"Autoimmune disease","subitem_subject_scheme":"Other"},{"subitem_subject":"Corticosteroid therapy","subitem_subject_scheme":"Other"},{"subitem_subject":"Cyclophosphamide","subitem_subject_scheme":"Other"},{"subitem_subject":"Hemophagocytic syndrome","subitem_subject_scheme":"Other"},{"subitem_subject":"Plasmapheresis","subitem_subject_scheme":"Other"}]},"item_language":{"attribute_name":"言語","attribute_value_mlt":[{"subitem_language":"eng"}]},"item_resource_type":{"attribute_name":"資源タイプ","attribute_value_mlt":[{"resourcetype":"journal article","resourceuri":"http://purl.org/coar/resource_type/c_6501"}]},"item_title":"Anti-MDA5 Antibody-positive Dermatomyositis Complicated by Autoimmune-associated Hemophagocytic Syndrome That Was Successfully Treated with Immunosuppressive Therapy and Plasmapheresis","item_titles":{"attribute_name":"タイトル","attribute_value_mlt":[{"subitem_title":"Anti-MDA5 Antibody-positive Dermatomyositis Complicated by Autoimmune-associated Hemophagocytic Syndrome That Was Successfully Treated with Immunosuppressive Therapy and Plasmapheresis"}]},"item_type_id":"2","owner":"2","path":["9"],"pubdate":{"attribute_name":"公開日","attribute_value":"2019-01-09"},"publish_date":"2019-01-09","publish_status":"0","recid":"1498","relation_version_is_last":true,"title":["Anti-MDA5 Antibody-positive Dermatomyositis Complicated by Autoimmune-associated Hemophagocytic Syndrome That Was Successfully Treated with Immunosuppressive Therapy and Plasmapheresis"],"weko_creator_id":"2","weko_shared_id":-1},"updated":"2023-05-16T04:01:25.555258+00:00"}