{"created":"2023-05-15T16:49:31.054515+00:00","id":27005,"links":{},"metadata":{"_buckets":{"deposit":"54b6f3bb-6c91-4d22-a7be-cc0fb71aa5b9"},"_deposit":{"created_by":6,"id":"27005","owners":[6],"pid":{"revision_id":0,"type":"depid","value":"27005"},"status":"published"},"_oai":{"id":"oai:nagasaki-u.repo.nii.ac.jp:00027005","sets":["10:11"]},"author_link":["120169","120177","120173","120176","120174","120171","120172","120170","120175"],"item_2_biblio_info_6":{"attribute_name":"書誌情報","attribute_value_mlt":[{"bibliographicIssueDates":{"bibliographicIssueDate":"2021-11-02","bibliographicIssueDateType":"Issued"},"bibliographicPageStart":"300569","bibliographicVolumeNumber":"26","bibliographic_titles":[{"bibliographic_title":"Human Pathology Reports"}]}]},"item_2_description_4":{"attribute_name":"抄録","attribute_value_mlt":[{"subitem_description":"Restrictive cardiomyopathy (RCM) is a rare type of primary myocardial disease, and its pathological features remain unclear. We report the case of a 78-year-old Japanese woman with RCM and MHY7 mutation who died of heart failure 13 years after the diagnosis. Upon autopsy, focal myocyte amorphous degeneration positive for ubiquitin was revealed, as well as myocardial disarrangement and interstitial fibrosis. Electron microscope demonstrated electron-dense structure in the cardiac myocytes. These may be one of the pathological features of RCM.","subitem_description_type":"Abstract"}]},"item_2_description_63":{"attribute_name":"引用","attribute_value_mlt":[{"subitem_description":"Human Pathology Reports, 26, art. no. 300569; 2021","subitem_description_type":"Other"}]},"item_2_publisher_33":{"attribute_name":"出版者","attribute_value_mlt":[{"subitem_publisher":"Elsevier B.V."}]},"item_2_relation_12":{"attribute_name":"DOI","attribute_value_mlt":[{"subitem_relation_type":"isIdenticalTo","subitem_relation_type_id":{"subitem_relation_type_id_text":"10.1016/j.hpr.2021.300569","subitem_relation_type_select":"DOI"}}]},"item_2_rights_13":{"attribute_name":"権利","attribute_value_mlt":[{"subitem_rights":"© 2021 The Author(s). Published by Elsevier Inc. This is an open access article under the CC BY-NC-ND license"}]},"item_2_source_id_7":{"attribute_name":"ISSN","attribute_value_mlt":[{"subitem_source_identifier":"2772736X","subitem_source_identifier_type":"ISSN"}]},"item_2_version_type_16":{"attribute_name":"著者版フラグ","attribute_value_mlt":[{"subitem_version_resource":"http://purl.org/coar/version/c_970fb48d4fbd8a85","subitem_version_type":"VoR"}]},"item_creator":{"attribute_name":"著者","attribute_type":"creator","attribute_value_mlt":[{"creatorNames":[{"creatorName":"Kawano, Hiroaki"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"Kawamura, Koichi"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"Kanda, Munetake"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"Ueki, Nozomi"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"Tanigawa, Muneo"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"Ishijima, Mitsuaki"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"Matsumoto, Yuji"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"Nakashima, Masahiro"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"Maemura, Koji"}],"nameIdentifiers":[{}]}]},"item_files":{"attribute_name":"ファイル情報","attribute_type":"file","attribute_value_mlt":[{"accessrole":"open_date","date":[{"dateType":"Available","dateValue":"2022-01-20"}],"displaytype":"detail","filename":"HPR26_300569.pdf","filesize":[{"value":"6.8 MB"}],"format":"application/pdf","licensetype":"license_note","mimetype":"application/pdf","url":{"label":"HPR26_300569.pdf","url":"https://nagasaki-u.repo.nii.ac.jp/record/27005/files/HPR26_300569.pdf"},"version_id":"60230ed5-0dc9-419d-b2ad-ee99e155545d"}]},"item_keyword":{"attribute_name":"キーワード","attribute_value_mlt":[{"subitem_subject":"Degeneration","subitem_subject_scheme":"Other"},{"subitem_subject":"Disarrangement","subitem_subject_scheme":"Other"},{"subitem_subject":"Fibrosis","subitem_subject_scheme":"Other"},{"subitem_subject":"Cardiomyopathy","subitem_subject_scheme":"Other"}]},"item_language":{"attribute_name":"言語","attribute_value_mlt":[{"subitem_language":"eng"}]},"item_resource_type":{"attribute_name":"資源タイプ","attribute_value_mlt":[{"resourcetype":"journal article","resourceuri":"http://purl.org/coar/resource_type/c_6501"}]},"item_title":"Autopsy of a patient with restrictive cardiomyopathy with and MYH7 mutation","item_titles":{"attribute_name":"タイトル","attribute_value_mlt":[{"subitem_title":"Autopsy of a patient with restrictive cardiomyopathy with and MYH7 mutation"}]},"item_type_id":"2","owner":"6","path":["11"],"pubdate":{"attribute_name":"公開日","attribute_value":"2022-01-20"},"publish_date":"2022-01-20","publish_status":"0","recid":"27005","relation_version_is_last":true,"title":["Autopsy of a patient with restrictive cardiomyopathy with and MYH7 mutation"],"weko_creator_id":"6","weko_shared_id":-1},"updated":"2023-05-15T20:03:41.416271+00:00"}