@article{oai:nagasaki-u.repo.nii.ac.jp:00027819,
 author = {Tokito, Takatomo and Sakamoto, Noriho and Ishimoto, Hiroshi and Okuno, Daisuke and Miyamura, Takuto and Hara, Atsuko and Kido, Takashi and Yamamoto, Kazuko and Yamaguchi, Hiroyuki and Obase, Yasushi and Akazawa, Yuko and Okamura, Ken and Suzuki, Tamio and Ishimatsu, Yuji and Mukae, Hiroshi},
 issue = {1},
 journal = {Internal Medicine},
 month = {Jan},
 note = {A 26-year-old Japanese woman was admitted with a 1-month history of diarrhea, a high fever for a few days, and exacerbation of dyspnea. She was treated with an antifibrotic drug and long-term oxygen therapy for Hermansky-Pudlak syndrome-related pulmonary fibrosis. New ground-glass attenuation appeared on chest computed tomography (CT), and a colon biopsy showed an inflammatory cell accumulation with a high titer of myeloperoxidase (MPO)-specific anti-neutrophil cytoplasmic antibodies (ANCA). Systemic inflammation related to MPO-ANCA titer elevation was suspected. Steroid pulse therapy and intravenous cyclophosphamide improved chest CT findings and diarrhea. Therefore, immunosuppressant treatment should be considered for systemic inflammation related to MPO-ANCA., Internal Medicine, 62(1), pp.103-106; 2023},
 pages = {103--106},
 title = {Pulmonary and Intestinal Involvement in a Patient with Myeloperoxidase-specific Antineutrophil Cytoplasmic Antibody-positive Hermansky-Pudlak Syndrome},
 volume = {62},
 year = {2023}
}